A CLASSIFICATION OF INFLAMMATORY DISORDERS
OF THE SKIN AND SUBCUTIS

  1. The Epidermis:
    1. Spongiotic dermatitis:
      1. Allergic contact dermatitis
      2. Photoallergic reactions
      3. Nummular eczema
      4. Superficial erythema annulare centrifugum
      5. Pityriasiform dermatitis, including:
        1. Pityriasis rosea
        2. Pityriasis lichenoides (spongiotic variant)
        3. Pityriasiform drug eruptions
      6. Giannott-Crosti
      7. Seborrheic dermatitis, acute
      8. Miliaria
      9. Stasis dermatitis
      10. Pruritic urticarial papules and plaques of pregnancy
      11. Eosinophilic spongiosis and its differential diagnosis, including:
        1. Incontinentia pigmenti
        2. Allergic contact reactions
        3. Pemphigus
        4. Pemphigoid
        5. Herpes gestationis
        6. Dermatitis herpetiformis
      12. Atopic dermatitis
      13. Drug reactions
      14. Polymorphous light eruption
      15. Perniosis
    2. Psoriasiform dermatitis:
      1. Psoriasis
      2. Seborrheic demraitits, chronic
      3. Pityriasis rubra pilaris
      4. Lichen simplex chronicus
    3. Interface dermatitis:
      1. Cell-poor vacuolopathic interface dermatitis
        1. Eosinophils absent
          1. Superficial vascular plexus injury present:
            • Dermatomyositis
            • Systemic lupus erythematosus, anti-Ro +ve
            • Sjogren's syndrome, anti-Ro/La +ve
            • Mixed connective tissue disease
          2. Superficial vascular plexus injury absent:
            • Systemic lupus erythematosus
            • Subacute cutaneous lupus erythematosus
            • Discoid lupus erythematosus (occasional case)
            • Relapsing polychondritis
            • Graft-versus-host disease, acute
            • Jessner's lymphocytic infiltrate (rare case)
            • Polymorphous light eruption (rare case)
            • Phototoxic eruptions
            • Erythema multiforme
        2. Eosinophils present
          1. Superficial vascular plexus injury present:
            • Dermatomyositis (occasional case, especially drug- or viral-related)
          2. Superficial vascular plexus injury absent:
            • Superficial erythema annulare centrifugum
            • Erythema multiforme
            • Delayed type hypersensitivity reaction (rare)
            • Graft-versus-host disease, acute (occasional)
            • Polymorphous light eruption (rare case)
            • Lupus erythematosus, drug-induced
            • Phototoxic eruptions
            • Erythema multiforme
      2. Lichenoid interface dermatitis
        1. Eosinophils absent:
          • Lichen planus
          • Subacute cutaneous lupus erythematosus
          • Discoid lupus erythematosus
          • Mixed connective tissue disease
          • Graft-versus-host disease, chronic
          • Delayed type hypersensitivity reactions, including
            • Insect bite reactions (occasional case)
            • Drug reactions (i.e. drug-iduced subacute lupus erythematosus)
          • Post-viral (i.e. post-Herpetic) eruptions
            • Lichenoid keratoses, including
            • Benign lichenoid keratosis
            • Lichenoid actinic keratosis
            • Lichenoid seborrheic keratosis
            • Porokeratosis
          • Pityriasis lichenoides
        2. Eosinophils present:
          • Delayed type hypersensitivity reactions, including
            • Insect bite reactions
            • Drug reactions, lichenoid (i.e. diuretics, antihypertensives, fixed drug eruptions)
            • Allergic contact reactions, lichenoid (i.e. photodevelopers)
            • Post-viral (i.e. post-Herpetic) eruptions
          • Lichenoid keratoses, including
            • Benign lichenoid keratosis
            • Lichenoid actinic keratosis
            • Lichenoid seborrheic keratosis
            • Porokeratosis
          • Graft-versus-host disease, chronic
  2. The Dermis:
    1. Lymphocytic dermal infiltrates (with minimal or no epidermal alteration)
      • Erythema annulare centrifugum (superficial and deep variant)
      • Delayed type hypersensitivity reactions, including
        • Insect bite reactions (rare case)
        • Dermal allergic contact reactions (i.e. nickel)
        • Atopic dermatitis
        • Drug reactions
      • Jessner's lymphocytic infiltrate, classical
      • Tumid lupus erythematosus
      • Steroid-treated connective tissue diseases of diverse types
      • Morphea and morpheiform tissue reactions
      • Malignant lymphoma, B-cell and T-cell types (angiotropic T-cell lymphoma, tumor stage mycosis fungoides, angioimmunoproliferative diseases)
      • Lymphomatoid connective tissue diseases
    2. Lymphocytic dermal infiltrates (with epidermal alteration)
      1. Eosinophils absent
        • Sjogren's syndrome (occasional case)
        • Mixed connective tissue disease
        • Systemic lupus erythematosus (rare case)
        • Discoid lupus erythematosus
        • Relapsing polychondritis
        • Jessner's lymphocytic infiltrate (rare case)
        • Polymorphous light eruption (superfical and deep variant)
        • Malignant lymphoma, T-cell type, including patch and early plaque-stage mycosis fungoides)
        • Pseudolymphoma, including:
          • Lymphomatoid connective tissue diseases
          • Persistant light reactors ("actinic reticuloid")
      2. Eosinophils present
        • Erythema multiforme
        • Delayed type hypersensitivity reaction (rare case)
        • Polymorphous light eruption (superfical and deep variant)
        • Lupus erythematosus, drug-induced
        • Malignant lymphoma, T-cell type, including late plaque stage and tumor stage mycosis fungoides)
        • Pseudolymphoma, including:
          • Lymphomatoid hypersensitivity reactions to:
            • Drugs
            • Insect bites (including "Woringer-Kolopp disease")
            • Contactants
            • Viruses (including herpetic infundibulofolliculitis)
            • Light ("actinic reticuloid")
    3. Histiocytic dermal infiltrates (with minimal or no epidermal alteration)
      1. Palisading necrotizing granulomatous dermatitis
        1. Necrobiosis lipoidica
        2. Granuloma annulare
        3. Rheumatoid nodule
        4. Juxta-articular nodes (spirchetal infection)
        5. Necrobiosis lipoidica-like tissue reactions in systemic disease
        6. Granuloma annulare-like tissue reactions in systemic disease
      2. Morphea and morpheiform tissue reactions
      3. Histiocytopathic drug reactions
      4. Histiocytopathies
    4. Histiocytic dermal infiltrates (with epidermal alteration)
      1. Histiocytopathic drug reactions
      2. Histiocytopathies related to mycoplasma, parvovirus, Epstein-Barr virus, and post-Herpetic eruptions
      3. Post-Streptococcal id reactions
      4. Connective tissue diseases with morpheiform tissue reactions, including:
        1. Lichen sclerosis/morphea overlap
        2. Lupus erythematosus
        3. Mixed connective tissue disease
    5. Neutrophilic/eosinophilic dermal infiltrates
      1. With epidermal alteration
        1. Pustular hypersensitivity states (i.e. drug eruptions, post-viral acropustulosis of infancy)
        2. Pustular follicular reactions, including
          1. Pyodermatous eosinophilic folliculitis
          2. Pyoderma gangrenosum
          3. Drug reactions (i.e. Dilantin hypersensitivity syndrome)
        3. Cellulitis
        4. Herpes gestationis
      2. Without epidermal alteration
        1. Urticaria
          1. Physical
          2. Neutrophilic
          3. Cholinergic
        2. Granuloma faciale
  3. The Subcutis:
    1. Septal panniculitis
      1. Erythema nodosum
      2. Morphea profunda
    2. Lobular panniculitis
      1. Erythema induratum (of Bazin)
      2. Lupus profundus and the other connective tissue diseases including:
        1. Behcet's disease
        2. Sjogren's syndrome
        3. Relpasing polychondritis
      3. Pancreatic panniculitis
      4. Weber-Christian disease
      5. Panniculitis of Rothman-Makai
      6. Factitial panniculitis
      7. Nodular vasculitis