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Placental Development, Indications for and Methods of Examination
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Section 4 -
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Infection

Phyllis C. Huettner, M.D.
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Intrauterine infections can have important consequences for the fetus including abortion,
stillbirth, active infection in the newborn period and long-term sequelae such as neurologic deficits
including cerebral palsy, mental retardation, blindness, deafness and learning disabilities.

There are two broad patterns of placental infection - ascending infections and hematogenous
infections, each associated with a characteristic type and pattern of inflammation within the placenta as
well as characteristic types of organisms. In general, ascending infections, the most common pattern,
are caused by bacteria that pass from the vagina or cervix into the uterus and cause acute inflammation
of the fetal membranes (acute chorioamnionitis) and umbilical cord (acute funisitis). In hematogenous
infections, a less common pattern, organisms are passed hematogenously from the mother to the placenta
and fetus. This pattern is typically due to viral organisms, protozoa (Toxoplasma
gondii) and some bacteria (Listeria monocytogenes, Treponema pallidum). The placenta usually shows chronic inflammation of the villi
(villitis). Infants may also be infected with bacterial or viral agents after passing through an
infected birth canal, a common form of infection with HIV and HSV, but this form of transmission does not
involve the placenta.

Ascending Infection and Acute Chorioamnionitis
Chorioamnionitis is the most common form of inflammation in the placenta. It is found in the
placentas of about 4% of uncomplicated term deliveries. Chorioamnionitis is strongly correlated with
prematurity and is increased in women of low socioeconomic status and African-American women.

It has become clear that infection causes acute chorioamnionitis. The implicated organisms
may be aerobic or anaerobic and are typically normal flora or contaminants of the vagina and cervix such
as Ureoplasma urealytica, Mycoplasma hominis, bacteroides urealyticus, E. coli, Staphylococci, Streptococci,
and Proteus. There is increasing evidence that some of these organisms
may ascend from the lower GYN tract weeks or even months before acute chorioamnionitis develops and
reside in the uterine tissues including the decidua due to decreased local immunity secondary to
pregnancy. Another common organism isolated from amniotic fluid is Fusobacterium
nucleatum, the organism seen in case 4.

Case 4: Acute Chorioamnionitis Secondary to Fusobacterium Infection
Microscopically this case is typical of severe necrotizing chorioamnionitis. There is a
marked acute inflammatory infiltrate that involves the chorion and the amnion. Extensive karyorrhectic
debris is present. The amniotic basement membrane is thickened and eosinophilic. Much of the amniotic
epithelium is necrotic or sloughed. Even on the H&E sections you can see numerous long, filamentous
organisms involving the amnion. This is an example of fusobacterium
chorioamnionitis.

Fusobacterium nucleatum is a gram-negative anaerobe that is
ubiquitous in the oral cavity and is associated with periodontal disease. Periodontal disease has
recently been recognized as a risk factor for preterm delivery. Fusobacterium
nucleatum has been cultured in the amniotic fluid of 10% to 30% of women in preterm labor with
intact membranes and in about 10% of women with preterm rupture of membranes. Yet this species of
fusobacterium is rarely isolated from the lower genital tract leading investigators to postulate that it
is dissemination, probably from oral plaque, that seeds the amniotic cavity. In experimental animals,
intravenous injection of Fusobacterium nucleatum colonizes and proliferates
in the uterus, beginning in the decidua and spreading to the chorion and amnion, eventually resulting in
preterm birth. The pathogenesis in humans is likely similar.

Pathologic Features and Grading of Acute Chorioamnionitis
On gross examination, the fetal membranes in chorioamnionitis are typically normal but in
cases of severe or longstanding infection, may be discolored, friable and foul smelling. Sometimes
small, white-yellow plaques can be seen on the surface of the umbilical cord when Candida is the etiologic agent.

Both the mother and the fetus (after about 20 weeks) respond to infection in the amniotic
cavity. Maternal neutrophils migrate from maternal blood vessels in the decidua, through the decidua,
the chorion and eventually into the amnion of the free membranes (membrane roll). Maternal neutrophils
also migrate from the intervillous space, which is essentially a maternal blood vessel, and accumulate in
the fibrin beneath the chorion, then pass through the connective tissue of the chorion and eventually
into the amnion of the fetal plate of the placenta. Fetal neutrophils migrate out of large vessels on
the chorionic plate on the side of the vessels closest to the amniotic cavity. In sections of the fetal
plate of the placenta, the inflammatory cells will be a mixture of maternal and fetal neutrophils.

Fetal neutrophils may also migrate from the umbilical cord vessels. The umbilical vein is
first involved, followed by the artery. Neutrophils are first seen in the clear spaces between smooth
muscle cells. Neutrophils may migrate completely through the vessel wall to involve the surrounding
Wharton's jelly. If severe, rings or arcs of degenerating neutrophils will surround the umbilical
vessels.

Because of the increasingly clear relationship between acute chorioamnionitis and adverse
fetal outcome, including long-term sequelae such as cerebral palsy and chronic lung disease, a
reproducible grading system has been proposed to facilitate standardization in diagnosis, study and
treatment. In this system both the stage (localization) and grade (severity) are determined for the
maternal inflammatory response (chorioamnionitis) and the fetal inflammatory response (chorionic
vasculitis and funisitis).

Usually bacteria are not seen on histologic sections. When they are, it is important to
consider post delivery overgrowth in unfixed specimens, especially those without inflammation. An
important exception is group B β-hemolytic streptococci which is such a
virulent organism that bacterial colonies may be found even without much inflammation. As we saw in the
Case 4, fusobacterium can also be visualized on H&E. Candida is another organisms identified on H&E, usually associated with
microabscesses on the surface of the umbilical cord (see below).

The pathogenesis of acute chorioamnionitis is likely different in term and preterm
gestations. In term gestations there is a strong relationship between rupture of membranes and the
duration of membrane rupture, and the likelihood of developing acute chorioamnionitis. In contrast, in
many preterm gestations, it appears that chorioamnionitis precedes and, in fact causes premature membrane
rupture and frequently preterm labor. In this situation, low virulence organisms such as Ureaplasma and Mycoplasma ascend into uterine
tissues, perhaps very early in pregnancy, and eventually extend from decidua to chorion, amnion and into
the amniotic fluid. Uterine contractions can be induced by inflammatory cytokines such as I-1, IL-6 and
tumor necrosis factor produced as a result of the inflammatory response. The inflammatory response also
releases other factors such as metalloproteases that degrade the extracellular matrix of the membranes
and remodel cervical collagen leading to premature cervical ripening and membrane rupture.

Peripheral Funisitis (Candida Infection)
Candida infections have a very
characteristic pattern of inflammation in the placenta. The typical finding has been referred to as
peripheral funisitis. Grossly, small, yellowish-white plaques, sometimes with a tan or red center, are
seen on the surface of the umbilical cord. Microscopically, wedge-shape abscesses are present just
beneath the amnion on the outer surface of the umbilical cord. Often the fungal and psuedo-hyphal forms
of the organisms can be appreciated on H&E sections but are even more apparent with special stains
like PAS or GMS. Occasional cases can show necrotizing funisitis in which there is abundant cellular
debris and sometimes calcification in the Wharton's jelly outside the umbilical vessels. Most cases of
Candida funisitis also have accompanying acute chorioamnionitis and fungal
organisms may be identified in the membranes.

Qureshi et al reported the largest series of Candida
funisitis, in which they studied 32 cases over a 14-year period. Seventy-five percent of their cases
were premature with a mean gestational age of 31 weeks. Only 16% of infants developed congenital
candidiasis, all with skin lesions at birth. Three of the mothers in this series had IUDs in place and
two had cerclages, known risk factors for developing intrauterine Candida
infection.

Hematogenous Infection
Infectious agents may reach the placenta by hematogenous spread from the mother. Usually
organisms that infect the placenta in this way are viruses but this pattern of spread may be seen with
some bacterial infections, such as Listeria and syphilis and parasitic
infections such as toxoplasmosis. Infections that reach the placenta by the hematogenous route are
usually associated with villitis. Villitis is usually not appreciated on gross examination of the
placenta. Occasionally, small foci of necrosis may be seen. Sometimes placentas with villitis are
enlarged and pale. Microscopically, there is an inflammatory infiltrate in the villi. The inflammatory
cells may be lymphocytes, histiocytes, plasma cells and, occasionally, neutrophils or a mixture of
these. Rarely, villitis may be composed of granulomatous inflammation. The inflammatory cells may be
associated with necrosis of the villous trophoblast and prominent villous agglutination with eosinophilic
fibrinoid material or they may infiltrate the villi without destruction. Sometimes the majority of the
inflammation is present around the villi (intervillositis). In addition to inflammation, the involved
villi may show vascular destruction, stromal hemosiderin and fibrosis. Usually areas of active
inflammation, resolving villitis and healed villitis are scattered in a patchy distribution throughout
the placenta. Sometimes, however, the villitis is localized to a particular area such as stem villi or
basal plate. This distribution does not appear to be related to the etiology.

Studies have shown that examination of four sections of placental parenchyma will detect the
vast majority of villitis, although in a more recent study six sections of parenchyma were required to
detect 85% of cases. Over 95% of villitis is villitis of unknown etiology (VUE, see below) meaning that
an infectious agent will not be identified on histologic sections, electron microscopy or culture. The
percentage of cases classified as VUE may change, however, as more advanced molecular techniques to
detect infection are applied to these cases. The morphologic features of some of the well known
infectious agents can sometimes point to a particular infectious etiology that may be confirmed with
immunohistochemistry, PCR, infant and maternal serologies, or detailed clinical history.

Case 5: CMV Villits

Cytomegalovirus
In the United States, CMV is the most commonly identified infectious agent in cases of
villitis where an etiology is identified. About 1% of infants are born with congenital CMV infection.
About 5% to10% of these will have disseminated disease with hepatosplenomegaly, jaundice, petechiae or
death. Ninety percent of congenitally infected infants will have clinically unrecognized disease and
about 5% to15% of these will have long-term sequelae such as mental retardation, learning disabilities
and sensorineural hearing loss. Congenital CMV infection represents an important public health problem.
It is estimated that nearly two billion dollars is spent annually in the U.S. on the care of symptomatic
infants with congenital CMV infection. Treatment of congenitally infected infants shortly after birth
may decrease the severity of neurologic damage and improve long-term outcome, therefore it is important
for pathologists to have a high level of suspicion for CMV and convey positive results immediately to the
pediatrician caring for the infant.

Grossly the placenta may be normal, small, if the fetus is growth retarded, or enlarged and
pale, if the fetus is anemic. The characteristic microscopic features of CMV villitis are
lymphoplasmacytic inflammatory infiltrates, stromal hemosiderin, necrotizing vasculitis, occluded villous
vessels and villous necrosis. In about 20% of cases the characteristic eosinophilic intranuclear and
basophilic cytoplasmic inclusions can be identified in stromal, endothelial, Hofbauer or trophoblast
cells. Immunohistochemistry, in situ hybridization and PCR will detect CMV in the placenta of cases of
congenital infection even in cases that are normal histologically or in which the infection is
subclinical. In a study of 94 term placentas sent for examination for reasons other than infection, that
were normal histologically, 11% had CMV detected by PCR and in situ hybridization. By in situ
hybridization, CMV DNA localizes predominantly in the mesenchyme and trophoblast of the villi but is also
seen in extravillous trophoblast and decidual cells.

CMV usually infects the fetus in utero. This may occur as a result of a primary maternal
infection during pregnancy, the pattern typically seen in women of higher socioeconomic status, or after
reactivation of latent viral infection, the pattern typical in women of lower socioeconomic status.
Primary maternal infection is more likely to infect the fetus and these fetuses are more likely to be
symptomatic. There is evidence that decidual cells or decidual macrophages may serve as a reservoir for
CMV and that reactivation from these cells is enhanced as a result of the inflammatory response to
concomitant bacterial infections.

Usually infected women are asymptomatic. There are no guidelines for treating CMV that occurs in
pregnancy, making the role of screening women for CMV infection unclear. Infection in the neonate may
also occur by contact with infected cervical secretions or, rarely, by an ascending route as well as by
hematogenous spread..

Herpes Simplex Virus (HSV)
Disseminated HSV infection may cause severe disease and death in the newborn. HSV is usually
acquired during delivery through an infected birth canal, but cases of transplacental and/or ascending
infection have also been reported. Hematogenous spread is uncommon but is associated with necrotizing
lymphocytic villitis or villous necrosis with little inflammation. Fibrinoid necrosis of villous vessels
has also been described. Recent work shows that placental factors serve as a barrier to vertical HSV
transmission. Syncytiotrophoblast cells show decreased expression of three HSV entry mediators needed
for virus to enter cells, effectively preventing access of HSV into the fetal circulation. Ascending
infection is associated with acute necrotizing chorioamnionitis, chronic lymphoplasmacytic
chorioamnionitis, or acute funisitis. Occasionally, viral inclusions may be seen in the amnion.
Immunohistochemistry and in situ hybridization may be helpful in confirming infection.

Varicella-Zoster
Because most women in the U.S. are infected during childhood, Varicella infection during
pregnancy is uncommon. About one-fourth of infants born to mothers with Varicella will be clinically
infected or show serologic evidence of infection. Only about 1% will develop the most severe
manifestations, congenital Varicella syndrome, characterized by cicatricial skin scarring, hypoplastic
limbs and ocular defects.

Infection is thought to occur transplacentally yet the majority of placentas are normal.
Some cases have been associated with villitis containing lymphocytes, plasma cells, histiocytes,
multinucleated giant cells and even poorly formed granulomas. Some have reported nuclear viral-like
inclusions in the villi. The decidua may show a lymphoplasmacytic infiltrate.

Parvovirus B19
Parvovirus B19 is a small single-stranded DNA virus that causes erythema infectiousum (Fifth
disease), a mild condition characterized by rash and low-grade fever, in children. Healthy adults are
usually asymptomatic but may develop polyarthralgia, arthritis or flu-like symptoms. People with sickle
cell disease or other chronic anemias may develop aplastic crises following infection.

About 50% of reproductive age women are immune to parvovirus. Of the non-immune women, about
17% will become infected after exposure. Exposure from a household contact, rather than occupational
exposure, results in the highest rate of maternal infection. Although most fetuses are unaffected by
maternal infection, the risk of fetal death is as high as 9% if infection occurs before 20 weeks
gestation. Most affected fetuses are hydropic and die between 20 and 28 weeks gestation. Infection with
parvovirus is a very uncommon cause of fetal loss in the first trimester. Whether parvovirus infection
may explain a significant number of late second trimester and third trimester non-hydropic losses is
controversial.

Parvovirus infects erythrocyte precursors, which have a specific receptor, as well as cardiac myocytes
and endothelial cells. Because erythropoesis is markedly increased in the second trimester, destruction
of erythroid precursors by parvovirus at this time leads to anemia and hydrops. Direct effects on
cardiac myocytes may also contribute. Parvovirus does not cause congenital anomalies.

As with fetal anemia of any cause, the placenta is often large for gestational age and pale.
The villi may be edematous and there is marked erythroblastosis. No villitis is seen. The red cell
precursors often contain eosinophilic intranuclear glassy inclusions that cause margination of the
chromatin. Similar inclusions can be seen in various fetal tissues especially bone marrow, liver and
lung. The inclusions are not well visualized in air-dried material (bone marrow smear or other tissue
smears). Immunohistochemistry, in situ hybridization and PCR may be useful in confirming the diagnosis.
Caution should be exercised in using PCR on placental tissue as this technique may amplify viremic
maternal blood and a positive result may not prove fetal infection.

Human Immunodeficiency Virus (HIV)
HIV can be transmitted from infected mother to infant in utero, by transplacental passage, at
delivery, or in the postnatal period by breastfeeding. Most cases of vertical transmission occur by
contact with maternal blood or secretions during delivery. The role the placenta plays in promoting or
preventing transmission of HIV is still not well understood. HIV antigens can be detected by
immunohistochemistry and in situ hybridization and HIV DNA by PCR in trophoblast, Hofbauer cells, villous
capillary endothelial cells and amnion, but these findings do not correlate well with the results of
viral culture or with infant infection.

The pathologic findings in placentas from HIV positive women have not shown a consistent
pattern. In one large study, the placentas of HIV positive women showed significantly more
chorioamnionitis and plasma cell deciduitis but were less likely than an HIV negative control group to
show villitis. In this study about 22% of the infants born to HIV positive women became infected.
Interestingly, the placentas of transmitting women in this study were significantly less likely to show
chorioamnionitis. Other studies have shown an association between maternal transmission and acute
chorioamnionitis and funisitis.

HIV is a tremendous public health problem in large parts of Africa as is malaria.
Co-infection with malaria and HIV has important implications for mother and infant. The frequency and
severity of malarial infections is increased in pregnant women who are HIV + compared to those that are
not. It is thought that this is due to the immunosuppression caused by HIV. These mothers have a
significantly greater chance of transmitting HIV to their children. Malaria in the placenta causes
significant placental inflammation and tissue destruction which may increase the access of maternal blood
to the fetal circulation. The rate of preterm delivery, low birthweight infants and infant mortality are
all significantly increased when these infections occur together.

Syphilis
The prevalence of congenital syphilis (CS) had risen dramatically in the 1980's and 1990's to
become the second most common cause of chronic intrauterine infection. Rates in the US fell dramatically
in the late 1990's but remain quite high in developing nations. The serologic diagnosis of syphilis in
the neonate is often problematic. The CDC requires the identification of spirochetes in fetal, neonatal,
cord or placental tissues to establish the diagnosis. For this reason, recognition of the placental
findings associated with CS is important in targeting cases for special stains and molecular studies.

On gross examination, placentas from cases of CS may be normal or may be enlarged, bulky and
edematous. Microscopically, many cases of CS exhibit the classic triad of 1). large, hypercellular,
immature villi 2). proliferative fetal vascular changes, characterized by endovascular proliferation
with lumen narrowing, perivascular fibroblastic proliferation with loosening and medial hypertrophy and
3). villitis, usually chronic, sometimes acute, plasmacytic or granulomatous. This triad is seen in
only 43%, two of three features in an additional 47% and only one of three in 10% of cases of CS. The
presence of intra or perivillous neutrophils in combination with proliferative vascular lesions is a
particularly good indicator of CS. In addition to the classic triad, some cases of CS are associated
with lymphoplasmacytic deciduitis and chorioamnionitis. Necrotizing funisitis, characterized by a band
of inflammation and karyorrhectic debris in the cord, is frequently seen in CS but is not specific. How
the pathologic findings in the placenta evolve over the course of in utero infection or change with
maternal treatment has not been studied.

Adding the pathologic placental features of congenital syphilis, particularly enlarged villi,
acute villitis and necrotizing funisitis, to the results of physical examination, long bone X-rays and
laboratory tests has been shown to improve the diagnosis of congenital syphilis from 67% to 89% in
live-born infants and 91% to 97% in stillborn infants in one study.

There is a strong association between the presence of the classic triad and spirochete
organisms on silver stains and Treponema pallidum DNA by PCR. Silver stains may also identify organisms even when the
complete triad is not present. In cases of CS the number of organism in the placenta, cord and membranes
may be quite low. It is often difficult to identify spirochetes in the villi, but when seen, they are
usually present in sclerotic villi adjacent to villitis. Organisms are best seen in the cord, free
membranes and decidua and may be identified even when these structures are not inflamed or abnormal. PCR
may identify additional cases not identified by staining.
 Listeria monocytogenes
The pathologic features of placentas in Listeria monocytogenes
infections are different in several respects from those of other villitides. With Listeria infection the predominant inflammatory cell is the neutrophil. These
gather between the trophoblast and villous stroma. Palisaded histiocytes and multinucleated giant cells
may also be seen. When several inflamed villi coalesce they form small microabscesses. These can
sometimes be seen as small white or yellow lesions on gross examination although generally the placenta
appears normal grossly. Usually there is also acute chorioamnionitis raising the possibility that the
infection may be spread by hematogenous and ascending mechanisms. Sometimes bacteria can be seen in
amniotic epithelial cells. The organism is a small rod-shaped or curved gram-positive bacillus.
Although difficult to visualize in tissue sections, it may stain with Warthin Starry, Dieterle or
Brown-Hopps stains. Recently work with an immunohistochemical stain suggests that this method may be
more sensitive than standard special stains.

The consequences of Listeria infection can be quite severe for
the fetus and neonate. Listeria may be a cause of spontaneous abortion,
prematurity, neonatal sepsis, meningitis, other morbidity and death. Perinatal infections are of two
types - early onset and late onset. Early onset infections typically occur within a few hours of
delivery and are associated with septicemia (85%) and respiratory disease (38%). This form has a high
mortality rate (30 to 63%) and is usually associated with a history of maternal disease and isolation of
Listeria monocytogenes from maternal sites. Late onset disease occurs five
or more days after delivery and is associated with septicemia and meningitis but has a lower mortality
rate (0 to 25%). Typically this pattern is not associated with a history of maternal illness and Listeria monocytogenes is not cultured from maternal sites.

Mothers become infected after ingesting food contaminated with Listeria, often an unpasteurized dairy product or unwashed vegetables. Most cases
are sporadic but epidemics do occur. Adults are usually not acutely ill but pregnant women develop a
febrile, flu-like illness and have a 20-fold increased incidence compared to other adults. The increased
severity of disease in pregnant women and the propensity to infect the fetus appears to be related to
decreased T cells and macrophages and ineffective macrophage function due to properties of the
endometrial stromal cells during pregnancy.
 Toxoplasma Gondii
The placental findings in Toxoplasma gondii infections are
highly variable. On gross examination, the placenta may be normal or enlarged and edematous.
Microscopically, villitis is usually seen but it may be subtle and non-necrotizing or extensively
necrotizing with fibrosis. Usually the inflammatory infiltrates are composed of lymphocytes and
histiocytes; plasma cells are not typically present. Sometimes true granulomas with central necrosis and
palisaded histiocytes are present in the inflamed villi. In addition to villitis, other findings include
decidual plasma cells, increased nucleated red cells in fetal vessels, a hemorrhagic endovasculitis-like
picture, chronic chorioamnionitis and funisitis, and thrombosis and calcification of large chorionic
vessels on the fetal plate.

Usually the encysted organism is the form that is identified in placental tissues. It may be
found in the cord, membranes, decidua or villi and may be difficult to identify, as the cysts are usually
not associated with inflammation. Tachyzoites released from the cysts are associated with marked
inflammation and necrosis. Immunohistochemistry, immunofluorescence and PCR may all aid in making the
diagnosis.

Congenital toxoplasmosis almost always occurs after primary maternal infection in pregnancy;
rare cases of infection after reactivation have been reported. In the U.S. only a third of adult women
are immune, therefore the majority of pregnant women are at risk for primary infection. This occurs from
ingesting oocyts from cat feces, soil or unwashed vegetables or tissue cysts from undercooked meat.
Transmission to the fetus occurs in 35 to 50% of primary maternal infections. The risk of transmission
increases the later in gestation the mother acquires the infection but the severity of sequelae in the
infant is increased if infection is acquired earlier in gestation. The majority of congenitally infected
infants are asymptomatic at birth but most will develop sequelae such as blindness, deafness,
microcephaly and decreased IQ. Because treatment during pregnancy as close to infection as possible
significantly reduces the number of infants with sequelae and the number with severe sequelae, there has
been intense interest in optimizing screening programs in areas with high rates of infection.

Villitis of Unknown Etiology (VUE)
The vast majority of cases of villitis represent villitis of unknown etiology (VUE) in which
an infectious etiology cannot be established. The incidence of VUE varies with the population studied
and ranges from 6% in a U.S. series to 26% in Argentina.

The placentas from most cases of VUE are normal on gross examination. Microscopically, about
85% are very mild or mild in extent meaning that six or fewer foci are identified in four sections of
placenta. In most cases the villitis is randomly distributed throughout the placenta but about 20% have
an exclusive or partial basal/parabasal distribution, often with associated decidual inflammation. Most
cases are necrotizing and are composed of lymphocytes and histiocytes. There may be associated
vasculitis of fetal stem vessels with associated downstream avascular terminal villi.

There are two schools of thought about the pathogenesis of VUE. One proposes that VUE is the
result of an as yet unidentified infectious pathogen. A diligent search for pathogens has been ongoing
for several decades now and no consistent patterns of infection have been detected in cases of VUE.
Recent studies, however, have examined selected patients with unexplained mortality or severe morbidity
such as unexplained acute systemic illness, respiratory death or neurologic compromise at birth, for
infectious agents. In situ hybridization was utilized to search for DNA viruses and RT-PCR utilizing a
bacterial concensus primer was used to search for bacterial organisms. In about 75% of these cases,
using these methods, an infectious etiology was found. The most common was Coxsackie virus. Villitis
was seen in only a minority of these cases however. Perhaps studies such as these, which utilize
molecular techniques to look for a wide variety of infectious agents, in cases of villitis of unknown
etiology would also find evidence of an infectious etiology.

Another theory proposes that VUE is an immunologic phenomenon. This seems more likely. The
cells in foci of villitis have been demonstrated to be primarily maternal in origin and to represent T
helper cells and Ia antigen-bearing macrophages as would be expected in an allograft reaction, in this
case host versus graft, between maternal and fetal tissues. This theory is also in keeping with clinical
features such as an increased incidence of maternal autoimmunity in women with placental VUE and the
tendency for VUE to recur in some patients in subsequent pregnancies. The target antigen of maternal
attack is still not known.

Although in most cases of VUE the fetus is unaffected, it has been significantly associated
with small for gestational age infants and antenatal growth arrest, perinatal mortality, oligohydramnios
not related to membrane rupture and to chronic monitoring abnormalities. These more severe clinical
complications are usually associated with more severe villitis. VUE is most commonly seen in placentas
from gestations over 32 weeks of age.

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